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KMID : 1144020190150010065
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Journal of Korean Association for Disability and Oral Health
2019 Volume.15 No. 1 p.65 ~ p.69
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DENTAL TREATMENT FOR A PATIENT WITH WOLF-HIRSCHHORN SYNDROME UNDER GENERAL ANESTHESIA: CASE REPORT
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Ryu Ji-Yeon
Song Ji-Soo
Shin Teo-Jeon
Hyun Hong-Keun
Kim Jung-Wook
Jang Ki-Taeg
Lee Sang-Hoon
Kim Young-Jae
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Abstract
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Wolf-Hirschhorn syndrome(WHS) is a congenital disorder caused by deletions of the short arm of chromosome 4. The most common characteristics are mental and growth retardation, dietary disorder and craniofacial features with a characteristic ‘Greek warrior helmet’ appearance. The dental characteristic of WHS includes delayed development, tooth agenesis, clefts, microdontia, taurodontism, and severely worn dentition. The purpose of this case report is to describe the dental treatment of a patient with WHS.
3-year-old boy with WHS visited the Seoul National University Dental Hospital for dental treatment. He had difficulty with nasotracheal intubation because of craniofacial anomalies and also had poor oral hygiene due to a limitation of mouth opening and dietary disorder. Due to his airway problem, behavior management and severity of dental conditions, dental treatment was performed under general anesthesia. This case suggests general anesthesia can be chosen with Wolf- Hirschhorn syndrome patients to safely care for their dental problems.
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KEYWORD
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Wolf-Hirschhorn syndrome, Dental treatment, General anesthesia, Oral manifestation
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